What are Isoleucine50 and Valine50 amino acid supplements?
Isoleucine50 and Valine50 are powdered amino acid supplements.
They are provided in convenient pre-measured sachets which are easy to use as no weighing or measuring is required.
Your dietitian will advise whether supplementation with Isoleucine50 or Valine50 is necessary for you or your child depending on individual requirements and blood levels of valine and isoleucine.
Who are Isoleucine and Valine amino acid supplements for?
The amino acids Isoleucine50 and Valine50 can be used from birth, right the way through childhood and into adulthood.
Why do I need to take Isoleucine and/or Valine?
In MSUD, if blood levels of the amino acids Valine and Isoleucine are too low, it then leads to higher leucine levels in the blood which is toxic. Therefore, it may be necessary to give some people with MSUD extra Valine and Isoleucine when they are well, particularly if they do not receive enough valine or isoleucine from their Leucine allowance (exchanges) from their diet.
In some cases, the amino acids Isoleucine50 and Valine50 may be added to the emergency feeds. These amino acids are likely to go low in the blood if they are not given from the daily Leucine allowance from food. During illness, it is commonly necessary to stop all Leucine exchanges from food to try and prevent Leucine reaching high levels in the blood.
Your dietitian will advise if Valine50 or isoleucine50 is necessary for you or your child based on individual requirements.
These supplements can be used alongside your MSUD protein substitute.
How much Isoleucine50 or Valine50 do I need?
The amount of Isoleucine50 or Valine50 needed will vary depending on a variety of factors including age and weight.
Your dietitian will tell you or your child exactly how much Isoleucine50 and/or Valine50 should be used and how often.
How do I use Isoleucine50 and Valine50?
Isoleucine50 and Valine50 can be used in a variety of ways, so your dietitian will advise you or your child on how they can be incorporated into your diet based on individual requirements.
What flavour are Isoleucine and Valine?
Isoleucine and Valine are unflavoured.
Isoleucine50 and Valine50 are foods for special medical purposes and should be use under strict medical supervision.